{"id":7073,"date":"2024-11-21T01:18:23","date_gmt":"2024-11-21T01:18:23","guid":{"rendered":"https:\/\/prrf.org\/?page_id=7073"},"modified":"2025-10-24T22:20:51","modified_gmt":"2025-10-24T22:20:51","slug":"pfvs","status":"publish","type":"page","link":"https:\/\/prrf.org\/zh\/pediatric-retinal-diseases\/pfvs\/","title":{"rendered":"\u80ce\u513f\u8840\u7ba1\u6301\u7eed\u7efc\u5408\u5f81\uff08PFVS\uff09"},"content":{"rendered":"
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Introduction and History<\/strong><\/p>\n

Persistent Fetal Vasculature Syndrome (PFVS) is a rare eye condition present at birth. It occurs when certain blood vessels in the eye, which are supposed to disappear before birth, remain and cause problems. These blood vessels are part of the “primary vitreous” and are meant to nourish the developing eye in the womb. If they don’t regress as they should, they can lead to vision issues.<\/p>\n

The condition was first clearly described in 1955 by an ophthalmologist named Dr. Algernon B. Reese, although he referred to it as “Persistent Hyperplastic Primary Vitreous” (PHPV). Dr. Morton F. Goldberg introduced the term \u201cpersistent fetal vasculature syndrome\u201d as the condition\u2019s new name in 1997.\u00a0 The preferred term is PFVS because it best describes the different ways the condition can appear.<\/p>\n

Who Is Affected?<\/strong><\/p>\n

PFVS usually affects one eye (unilateral) but can sometimes affect both eyes (bilateral). It’s present at birth and is often noticed when a baby has a white spot in the eye (leukocoria). PFVS can occur in children with no other health problems, but in some cases, it may be linked to other conditions.<\/p>\n

Diagnosis<\/strong><\/p>\n

Often, parents or a pediatrician might notice something unusual about the baby’s eye, such as:<\/p>\n

An ophthalmologist, a specialist in eye care, will conduct a comprehensive eye exam. They might use special lights and magnifying tools to examine the inside of the eye. To get a better view of the back of the eye and the leftover vessels, they often use:<\/p>\n